Severe Vestibulocochlear Involvement in Wegener’s Granulomatosis: A Rare Presentation Afectación vestibulococlear grave en granulomatosis de Wegener localizada: una presentación atípica
نویسندگان
چکیده
We present the clinical case of 61-year-old female, lacking relevant antecedents, whose condition began with tinnitus and hearing loss of the right ear (RE). At 4 months she presented an episode of sudden vertigo, followed by continuous dizziness and imbalance. She received a diagnosis of otitis media with effusion (OME), but did not improve after various treatments. After that, she developed hearing loss of the left ear, with a sensation of fluctuating blockage, tinnitus and right facial paresis. One year later, the hearing loss had progressed toward bilateral cophosis and the imbalance worsened. However, the facial paralysis facial subsided. Otomicroscopy exploration: image compatible with OME. Ear and neurological examination: no spontaneous nystagmus, Halmagyi test with corrective ocular with saccades on both sides, instability in Romberg and Unterberger test, absence of response to caloric stimulation (even with ice water) and in the kinetic vestibular rotating chair test (at both low and intermediate frequencies), the patient presented only minimal response to high frequency stimulation, with a gain of merely 0.12--0.64 Hz of rotation. Imaging
منابع مشابه
Bilateral Facial Paralysis and Otitis Media as the First Presentations of Wegener’s Granulomatosis: A Case Report
Introduction: Cranial nerve palsy in Wegener’s granulomatosis is a curious incident, particularly if it occurs without kidney or lung involvement. In a review of medical articles, only 1 case of Wegener’s granulomatosis with bilateral facial nerve palsy was found. Case Presentation: The patient was a 16-year-old female who presented with pain and hearing ...
متن کاملUnilateral eyelid edema and mucosal involvement as the first presentations of Wegener granulomatosis
Background: Wegener granulomatosis or granulomatosis with polyangiitis is a pauci-immune small vessel vasculitis which is usually associated with anti-neutrophil cytoplasmic antibodies (ANCA) mainly in old men. This small vessel vasculitis is usually characterized by necrotizing granulomatous inflammation with multiorgan involvement. Kidneys could be involved as the main and life-threatening co...
متن کاملWegener Granulomatosis with Oral Involvement as Primary Manifestation: A Case Study
Introduction: Wegener Granulomatosis is a rare multisystemic disease with an unknown cause, characterized by necrotic granulomatous lesions in respiratory tract, systemic vasculitis in small arteries and veins and necrotizing glomerulonephritis. Wegener can affect any organ including kidneys, eyes or other organs but classically affects upper and lower respiratory tract. One of the rare but imp...
متن کاملWegener’s Granulomatosis Presenting with Bilateral Facial Nerve Palsy and Limited to the Head and Neck
Objectives. To illustrate the only reported case of Wegener’s granulomatosis limited to the head and neck, and to provide an update on current knowledge and treatment of Wegener’s granulomatosis. Case report. A 50-year-old man presented with bilateral chronic otitis and mastoiditis, eventually developing bilateral facial palsies. While he progressed with other head and neck symptoms, his diseas...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
دوره شماره
صفحات -
تاریخ انتشار 2017